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ABCD2

ATP-binding cassette, sub-family D (ALD), member 2

Synonyms:
ABC39, ALDL1, ALDR, ALDRP, hALDR
Species:
UniProtKB ID:
Gene ID:
  • Human(225) Summary: The protein encoded by this gene is a member of the superfamily of ATP-binding cassette (ABC) transporters. ABC proteins transport various molecules across extra- and intra-cellular membranes. ABC genes are divided into seven distinct subfamilies (ABC1, MDR/TAP, MRP, ALD, OABP, GCN20, White). This protein is a member of the ALD subfamily, which is involved in peroxisomal import of fatty acids and/or fatty acyl-CoAs in the organelle. All known peroxisomal ABC transporters are half transporters which require a partner half transporter molecule to form a functional homodimeric or heterodimeric transporter. The function of this peroxisomal membrane protein is unknown; however this protein is speculated to function as a dimerization partner of ABCD1 and/or other peroxisomal ABC transporters. Mutations in this gene have been observed in patients with adrenoleukodystrophy, a severe demyelinating disease. This gene has been identified as a candidate for a modifier gene, accounting for the extreme variation among adrenoleukodystrophy phenotypes. This gene is also a candidate for a complement group of Zellweger syndrome, a genetically heterogeneous disorder of peroxisomal biogenesis. [provided by RefSeq, Jul 2008]
  • Mouse(26874) ATP-binding cassette, sub-family D (ALD), member 2
  • Rat(84356) ATP-binding cassette, subfamily D (ALD), member 2
  • sheep(101119199) ATP-binding cassette, sub-family D (ALD), member 2
  • naked mole-rat(101706287) ATP-binding cassette, sub-family D (ALD), member 2
  • domestic guinea pig(100715583) ATP-binding cassette, sub-family D (ALD), member 2
  • Zebrafish(100537809) ATP-binding cassette, sub-family D (ALD), member 2
  • chicken(417694) ATP-binding cassette, sub-family D (ALD), member 2
  • dog(477643) ATP-binding cassette, sub-family D (ALD), member 2
  • cow(526436) ATP-binding cassette, sub-family D (ALD), member 2
  • domestic cat(101095424) ATP-binding cassette, sub-family D (ALD), member 2

Custom & Knockdown Gene Products

esiRNA

Product Number
Description
Species
MISSION® esiRNA, targeting human ABCD2,
Species
human
MISSION® esiRNA, targeting mouse Abcd2,
Species
mouse