ERCC6
excision repair cross-complementing rodent repair deficiency, complementation group 6
Synonyms:
ARMD5, CKN2, COFS, COFS1, CSB, RAD26, UVSS1 
Species:
Human ERCC6 (2074), Mouse Ercc6 (319955), Rat Ercc6 (306274), naked mole-rat Ercc6 (101712293), Horse ERCC6 (100062916), sheep ERCC6 (101117559), domestic guinea pig Ercc6 (100719487), chicken ERCC6 (423785), Zebrafish ercc6 (560477), domestic cat ERCC6 (101092399) ...More
UniProtKB ID:
Gene ID:
- Human(2074) Summary: This gene encodes a DNA-binding protein that is important in transcription-coupled excision repair. The encoded protein has ATP-stimulated ATPase activity, interacts with several transcription and excision repair proteins, and may promote complex formation at DNA repair sites. Mutations in this gene are associated with Cockayne syndrome type B and cerebrooculofacioskeletal syndrome 1. Naturally-occurring readthrough transcription occurs between this gene and the adjacent PGBD3 gene (GeneID:267004), and results in a fusion protein that shares sequence with the product of each individual gene. The readthrough locus is represented by GeneID:101243544. [provided by RefSeq, Mar 2013]
- Mouse(319955) excision repair cross-complementing rodent repair deficiency, complementation group 6
- Rat(306274) excision repair cross-complementing rodent repair deficiency, complementation group 6
- naked mole-rat(101712293) excision repair cross-complementing rodent repair deficiency, complementation group 6
- Horse(100062916) excision repair cross-complementing rodent repair deficiency, complementation group 6
- sheep(101117559) excision repair cross-complementing rodent repair deficiency, complementation group 6
- domestic guinea pig(100719487) excision repair cross-complementing rodent repair deficiency, complementation group 6
- chicken(423785) excision repair cross-complementing rodent repair deficiency, complementation group 6
- Zebrafish(560477) excision repair cross-complementing rodent repair deficiency, complementation group 6
- domestic cat(101092399) excision repair cross-complementing rodent repair deficiency, complementation group 6
- dog(477747) excision repair cross-complementing rodent repair deficiency, complementation group 6
- cow(522908) excision repair cross-complementing rodent repair deficiency, complementation group 6
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Antibodies
Product Number
Description
Species Reactivity
Application
Anti-ERCC6 antibody produced in rabbit, affinity isolated antibody, buffered aqueous solution, 
Species Reactivity
human, mouse, rat 
Application
immunofluorescence
immunohistochemistry
immunoprecipitation (IP)
western blot
immunohistochemistry
immunoprecipitation (IP)
western blot
Anti-CSB (ERCC6) Antibody, clone ICSB-3H8, clone 1CSB-3H8, from mouse, 
Species Reactivity
human 
Application
ChIP
flow cytometry
immunocytochemistry
immunoprecipitation (IP)
western blot
flow cytometry
immunocytochemistry
immunoprecipitation (IP)
western blot
Anti-ERCC6 antibody produced in rabbit, Prestige Antibodies® Powered by Atlas Antibodies, affinity isolated antibody, 
Species Reactivity
human 
Application
immunofluorescence