产品名称
谷氨酰-L-肉碱 锂盐, ≥98.0% (TLC)
Quality Segment
assay
≥98.0% (TLC)
form
solid
optical activity
[α]/D -20±2°, c = 1 in H2O
impurities
≤10% water
color
white to off-white
storage temp.
2-8°C
SMILES string
C[N+](C)(C)C[C@H](OC(CCCC(O)=O)=O)CC([O-])=O.C
InChI
1S/C12H21NO6/c1-13(2,3)8-9(7-11(16)17)19-12(18)6-4-5-10(14)15/h9H,4-8H2,1-3H3,(H-,14,15,16,17)/t9-/m1/s1
InChI key
NXJAXUYOQLTISD-SECBINFHSA-N
Biochem/physiol Actions
戊二酰肉碱的形成和排泄升高是戊二酰辅酶A脱氢酶缺乏症所导致的结果,而这是一种赖氨酸和色氨酸代谢的先天性错误。由于戊二酰肉碱的形成和尿排泄升高所引起的继发肉碱消耗可能在戊二酰辅酶A脱氢酶缺乏症的神经病变中起重要作用,从而诱发兴奋性神经毒性和线粒体功能障碍。
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存储类别
11 - Combustible Solids
wgk
WGK 3
flash_point_f
Not applicable
flash_point_c
Not applicable