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Merck
CN

Renal transport of aromatic acids in patients with phenylketonuria.

Journal of inherited metabolic disease (1981-01-01)
U Langenbeck, A Behbehani, H Luthe
摘要

Renal clearance of phenylpyruvic acid is maximal at a plasma concentration of 40-60 mumol/l. This concentration is obtained with plasma phenylalanine concentrations of 1.0-1.2 mmol/l, the threshold for separating classical phenylketonuria from phenylketonuria variants.

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